Disease Management

You should discuss the risks and benefits of any management options or procedure with your physician.

Supportive and symptom-based management

Since MPS I is a multi-systemic disease, care of an MPS I patient can involve many specialists. Patients with MPS I may require supplemental oxygen, continuous positive airway pressure, or tracheostomy for breathing difficulties. Surgery may be necessary for spinal cord compression, hernia repair, carpal tunnel syndrome, or heart valve replacement. Physical therapy can help with joint stiffness.

Disease-Specific Management

Ask your doctor if disease-specific management options and procedures may be right for you and discuss their risks and benefits.